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Aortopathies Panel

A 29-gene panel for evaluating inherited aortopathy, including thoracic aortic aneurysms and dissections (TAAD) and Marfan Syndrome, powered by the Helix Exome+® platform.

Turnaround

6-21 days

Turnaround Requery

≤ 5 days

Panel Description

This panel evaluates 29 genes associated with inherited aortopathy and related conditions. Genes included are associated with isolated thoracic aortic aneurysms and dissections (TAAD), Marfan Syndrome, and conditions which may include aortopathy as one feature.

Have Questions?

Our team is available Monday through Friday, 9am-5pm Pacific Time.

Indications for Testing

A relevant personal and/or family history suggestive of an inherited aortopathy.

Methodology

This test utilizes next-generation sequencing to detect single nucleotide variants, insertions and deletions up to 20 bp, and copy number variants in genes associated with inherited aortopathy and related conditions.

Technical Specifications

Analytical sensitivity (SNV)

> 99%

Analytical sensitivity (indel)

> 99%

Analytical specificity

> 99%

CNV sensitivity (multi-exon)

> 99%

CNV sensitivity (single-exon)

> 90%

Gene notes

FOXE3: Analysis begins at chr1:47416567 (GRCh38) and excludes the first quarter of exon 1. TGFBR1: Analysis for exon 1 will not be performed....

Genomic build

GRCh38

Genes Tested

ACTA2
ADAMTS10
BGN
CBS
COL3A1
COL5A1
COL5A2
EFEMP2
FBN1
FBN2
FLNA
FOXE3
LOX
MED12
MFAP5
MYH11
MYLK
NOTCH1
PLOD1
PRKG1
SKI
SLC2A10
SMAD2
SMAD3
SMAD4

Showing 25 of 29 genes in this panel

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