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Aortopathies Panel

A 29-gene panel for evaluating inherited aortopathy, including thoracic aortic aneurysms and dissections (TAAD) and Marfan Syndrome, powered by the Helix Exome+® platform.

Turnaround

6-21 days

Requery (SOQO)

≤ 5 days

Genes Tested

29

Panel Description

This panel evaluates 29 genes associated with inherited aortopathy and related conditions. Genes included are associated with isolated thoracic aortic aneurysms and dissections (TAAD), Marfan Syndrome, and conditions which may include aortopathy as one feature.

Order This Test

Contact our clinical team to order this panel or learn more.

(855) 699-1933
clinicalsupport@helix.com

Indications for Testing

A relevant personal and/or family history suggestive of an inherited aortopathy.

Methodology

This test utilizes next-generation sequencing to detect single nucleotide variants, insertions and deletions up to 20 bp, and copy number variants in genes associated with inherited aortopathy and related conditions.

Technical Specifications

Analytical sensitivity (SNV)

> 99%

Analytical sensitivity (indel)

> 99%

Analytical specificity

> 99%

CNV sensitivity (multi-exon)

> 99%

CNV sensitivity (single-exon)

> 90%

Gene notes

FOXE3: Analysis begins at chr1:47416567 (GRCh38) and excludes the first quarter of exon 1. TGFBR1: Analysis for exon 1 will not be performed.

Genomic build

GRCh38

Genes Tested

29 genes included in this panel

ACTA2ADAMTS10BGNCBSCOL3A1COL5A1COL5A2EFEMP2FBN1FBN2FLNAFOXE3LOXMED12MFAP5MYH11MYLKNOTCH1PLOD1PRKG1SKISLC2A10SMAD2SMAD3SMAD4TGFB2TGFB3TGFBR1TGFBR2

Ordering Information

Turnaround Time

Typically 6-21 days (standard), Typically ≤ 5 days (requery)

Preferred Specimen

BD Vacutainer Whole Blood K2 EDTA Collection Tube 4mL or Oragene Dx Saliva Collection Kit

Shipping Instructions

Specimens to arrive at Helix within 96 hours of collection at ambient temperature.

Clinical Description

This panel evaluates 29 genes associated with inherited aortopathy and related conditions. Genes included are associated with isolated thoracic aortic aneurysms and dissections (TAAD), Marfan Syndrome, and conditions which may include aortopathy as one feature.

Ready to order this test?

Contact our clinical team to order the Aortopathies Panel for your patients.